Bleeding Disorders and Treatment
How the NHS commissions services for rare bleeding disorders
Haemophilia, von Willebrand’s disease and other bleeding disorders affect relatively few people but require a high level of clinical expertise and treatment with expensive drugs.
Achieving Haemostasis
Strategies for the drug treatment of haemophilia and VWD depend on the risk of bleeding. For haemophilia, replacement FVIII is the treatment of choice for prophylaxis and acute treatment of bleeding Desmopressin may be preferred for patients with mild or moderate haemophilia A when FVIII can be raised to an appropriate therapeutic level; in such …
Care of Bleeding Disorder Patients
The primary aim of care is to prevent and treat bleeding with the deficient clotting factor but optimal care requires more than the treatment of acute events. The following recommendations are based on WFH guidelines [WFH, 2013] but the principles of management are similar for VWD [Laffan et al, 2014]. Comprehensive care People with bleeding …
Bleeding Disorders 101
Congenital bleeding disorders are characterised by impaired blood clotting, usually due to an inherited deficiency in or abnormal functioning of a clotting factor. There are many types (depending on which clotting factor is affected) but, with three exceptions, they are rare. The major bleeding disorders The most frequent bleeding disorders are haemophilia A, haemophilia B …